C96.0: Multifocal and multisystemic (disseminated) Langerhans-cell histiocytosis [Letterer-Siwe disease]

You have cancer in certain immune cells.

There are various kinds of defense cells (immune cells) in the body. Specific immune cells produce antibodies in the blood. The antibodies cling to pathogens and foreign substances in the blood, for example. This allows the antibodies to make the pathogens and foreign substances visible to the immune system. The immune system helps the body to fight and eliminate diseases and foreign substances.

In your case, the cancer of specific immune cells developed in a short time. Often you are then suddenly seriously ill. You can then have fever and the lymph nodes in the body can swell up. The lymph nodes are small bean-shaped objects. They are found throughout the body. Lymph nodes filter the tissue fluid. They are part of the defense system. Several organs such as bones, the liver or the lungs are often affected at the same time. The bones of the head or the legs, for example, can be especially destroyed by this cancer. Areas of the skin are usually reddened and flaky. The disease usually develops in infancy.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information

Note

This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.

Source

Provided by the non-profit organization “Was hab’ ich?” gemeinnützige GmbH on behalf of the Federal Ministry of Health (BMG).