E84.0: Cystic fibrosis with pulmonary manifestations

You have cystic fibrosis.

With cystic fibrosis, the genetic information for a particular protein is changed. When beginning its development, every single cell in the body contains a complete blueprint of the body. This blueprint consists of genetic information. The genetic information is encrypted in the chromosomes. Every human cell normally contains 23 chromosome pairs, i.e. a total of 46 chromosomes. Cystic fibrosis can be hereditary. Family members can also be affected.

When the genetic information changes, that particular protein does not work properly. The body needs the protein to produce certain fluids. If the protein does not work properly the phlegm in the lungs and intestine or the pancreatic juice can become very viscous, for example. This can cause organs to get blocked and damaged. Because of the cystic fibrosis you are having problems with your lungs.

The lungs are on the left and right side of the ribcage. They are also connected to the nose and mouth via the bronchial tubes and windpipe (trachea). You need lungs to breath. When we breathe in, oxygen enters the lungs and accumulates in the blood. This blood then flows to the heart. The heart then pumps the oxygen-rich blood throughout the body. All of the organs are supplied with oxygen as a result. Air enters the lungs through the airways. The lower airways begin with the trachea (windpipe) and continue into the lungs. The airways branch out further into the lungs, becoming smaller and smaller.

It can be difficult to cough up the viscous phlegm. The phlegm can damage the airways. The lungs may then keep getting inflamed and they can become more vulnerable to pathogens. The pathogens may then cause the lung inflammation to be long-lasting. This circulation can result in the lungs being permanently inflamed. This can lead to breathlessness and make you less resilient physically. If the lungs are severely damaged, the heart may also be damaged.

You may only have a few symptoms or be very sick. That depends on how much of the altered protein you have.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information


This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.


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