Q43.1: Hirschsprung disease

The nerves in your intestines have not developed fully. This defect is congenital, which means you were born with it.

The intestines are like a tube. There is a hollow space on the inside. The intestinal wall lies around this hollow space.

The intestine develops before birth. Nerves grow into the intestinal wall at this stage. The nerves are important because they affect the movements of the intestines. The intestines alternately contract and relax. These movements carry the stool forward through the intestines.

In your case, the nerves in the intestinal wall have not developed fully. The last part of the intestines is usually affected by this. However, other sections of the intestines may be affected, too. This results in strong contractions of the affected part of the intestines. This can produce various symptoms. It sometimes takes a long time for a baby to pass stools after birth, for example. Difficulty passing stools may also be experienced later. In some cases, so much stool may build up in the intestines that it becomes very wide. This can result in the intestines becoming inflamed.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information


This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.


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