Q56.1: Male pseudohermaphroditism, not elsewhere classified

Your external genital organs resemble female genital organs, although your biological sex is male.

The X chromosome and the Y chromosome determine a person’s biological gender. Men normally have one X chromosome and one Y chromosome. Women normally have 2 X chromosomes.

While developing in the womb, many different types of tissue develop in the body. The organs and body parts develop out of the various types of tissue. The internal and external genital organs also develop during the time in the womb. Male and female sex hormones are important for the development of the genital organs.

Your external genital organs resemble female genital organs. This can happen even though the biological sex is male and testicles have developed.

There can be various reasons for genital organs not developing in accordance with biological sex. It may be, for example, that the male sex hormones are not produced as they normally are. Certain tissues in the body may also not properly respond to the male sex hormones.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information

Note

This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.

Source

Provided by the non-profit organization “Was hab’ ich?” gemeinnützige GmbH on behalf of the Federal Ministry of Health (BMG).