Q82.00: Hereditary lymphoedema of upper and lower extremity(ies), stage I

Your lymph vessels have not developed properly. This condition is congenital, which means you were born with it.

Fluid forms in tissue throughout the body every day. This tissue fluid is the lymph. The lymph is carried around the body by lymph vessels. The lymph vessels run around the entire body and are connected to blood vessels. At some points, there are lymph nodes along the lymph vessels. Pathogens are rendered harmless in the lymph nodes, for example.

The disorder is hereditary. Other family members may also be affected. In some cases, other organs have also failed to develop properly.

If the lymph vessels have not developed properly, lymphatic fluid may build up in the body. The lymph has accumulated in your arms or legs.

If you press on the parts of the skin that are affected, you can briefly press aside the lymph below. This causes a dent to form in that place for a short time. Raising the affected body parts reduces the swelling. The raising enables the lymph to drain away better.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information

Note

This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.

Source

Provided by the non-profit organization “Was hab’ ich?” gemeinnützige GmbH on behalf of the Federal Ministry of Health (BMG).