Q87.0: Congenital malformation syndromes predominantly affecting facial appearance

You have a congenital disorder that has resulted in a change to your face, among other things.

This congenital disorder has meant that parts of your body have not developed properly, if at all. The condition can be hereditary. The condition can also affect other family members.

Various hereditary diseases can lead to a change in the face. For example, individual parts of the face may fail to form properly. The bones of the cranium or jaw can also be changed. The disorder may also affect other parts of the body or organs, such as the heart.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information


This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.


Provided by the non-profit organization “Was hab’ ich?” gemeinnützige GmbH on behalf of the Federal Ministry of Health (BMG).