D64.4: Congenital dyserythropoietic anaemia

You don’t have enough haemoglobin or red blood cells in your blood.

Blood is made up of blood plasma and blood cells. The blood cells also include red blood cells. They contain haemoglobin, the pigment that gives the blood its red color. This pigment is important for carrying oxygen in the blood.

Either your haemoglobin or your red blood cells are not being formed correctly. This condition is congenital, which means you were born with it.

Your red blood cells are not working properly. They may also be more quickly broken down by the body than normal. This gives the liver and spleen too much to do. As a result, you can have a spleen or liver that is too big. The breakdown products of the red blood cells can be deposited in the skin. This can make the skin look yellow.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information


This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.


Provided by the non-profit organization “Was hab’ ich?” gemeinnützige GmbH on behalf of the Federal Ministry of Health (BMG).