Q80.2: Lamellar ichthyosis

You have a congenital disorder that makes your skin red and flaky.

The top of layer of skin is made up of skin cells that are keratinized. These skin cells are initially in one of the lower skin layers. When the skin cells migrate upwards toward the skin’s surface, they keratinize, forming a solid layer.

The genetic information in your cells has changed. This disrupts the keratinization of your skin.

There are various forms of this condition. Some forms cause the skin to be red and flaky after birth. You can get colder than usual or lose fluid through the skin. The skin can become inflamed more easily than usual and large wounds can form. With other forms there is a firm layer all over the skin or on large parts of the skin. You may also have other symptoms.

The symptoms can change or disappear completely when one is older. You can get brownish scaly skin or firm patches on the skin.

This disease is hereditary. Other family members may also be affected.

Additional indicator

On medical documents, the ICD code is often appended by letters that indicate the diagnostic certainty or the affected side of the body.

  • G: Confirmed diagnosis
  • V: Tentative diagnosis
  • Z: Condition after
  • A: Excluded diagnosis
  • L: Left
  • R: Right
  • B: Both sides

Further information


This information is not intended for self-diagnosis and does not replace professional medical advice from a doctor. If you find an ICD code on a personal medical document, please also note the additional indicator used for diagnostic confidence.
Your doctor will assist you with any health-related questions and explain the ICD diagnosis code to you in a direct consultation if necessary.


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